OUTCOMES IN PATIENTS WITH DEE-SWAS TREATED WITH HORMONAL THERAPY IN COMBINATION WITH CLOBAZAM: PROSPECTIVE STUDY DATA

Шохимардонов Шохижахон Шохимардонович, Туйчибаева Нодира Мираталиевна

Журнал неврологии и нейрохирургических исследований / Journal of Neurology and Neurosurgical Research · 2026-yil

Annotatsiya

Developmental and epileptic encephalopathies with spike–wave activation in sleep (DEE-SWAS, formerly known as CSWS/ESES) represent a severe form of epilepsy characterized by neurodevelopmental regression, behavioral disturbances, speech impairment, and cognitive deficits. The key neurophysiological hallmark of the syndrome is pronounced epileptiform activity during slow-wave sleep with a high spike–wave index (SWI). Higher SWI values correlate with more severe clinical regression, and the duration of untreated sleep-activated epileptiform activity is directly associated with cognitive decline. To date, hormonal therapy (corticosteroids or ACTH) is considered the most effective treatment option; however, optimal treatment regimens and therapeutic combinations require further investigation. Clobazam, a benzodiazepine anticonvulsant with proven efficacy in DEE-SWAS, is frequently used as part of polytherapy. Nevertheless, data on combined treatment with hormonal therapy and clobazam in Central Asian populations are scarce.

Maqola ma’lumotlari
MualliflarШохимардонов Шохижахон Шохимардонович, Туйчибаева Нодира Мираталиевна
JurnalЖурнал неврологии и нейрохирургических исследований / Journal of Neurology and Neurosurgical Research
Nashr sanasi2026-01-05
Jild6
Son6/2
TilRus

Kalit so‘zlar

DEE-SWAS, Эпилептическая энцефалопатия, Эпилепсия, Гормональная терапия, Клобазам, DEE-SWAS, epileptic encephalopathy, epilepsy, hormonal therapy, clobazam, DEE-SWAS, epileptic encephalopathy, epilepsy, hormonal therapy, clobazam

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