CLINICAL AND DIAGNOSTIC FEATURES OF HYPERANDROGENISM IN MAYER-ROCKTANSKY-KUESTER-HAUSER SYNDROME

Адылова М.Н, Негмаджанов Б.Б, Раббимова Г.Т

Journal of reproductive health and uro-nephrology research (Репродуктив саломатлик ва уро-нефрологик тадқиқотлар журнали) · 2022-yil

Annotatsiya

Congenital uterine-vaginal aplasia or Mayer-Rokitansky-Kuester-Hauser syndrome (MRKH) is characterized by ungrown uterine buds, cervical and vaginal aplasia, but normal or hypoplastic bilateral appendages and clinically manifests as primary amenorrhea. Patients with MRKH have a normal female phenotype and karyotype development (46, XX) and an incidence of 1 per 4,000 or 5,000 newborns

Maqola ma’lumotlari
MualliflarАдылова М.Н, Негмаджанов Б.Б, Раббимова Г.Т
JurnalJournal of reproductive health and uro-nephrology research (Репродуктив саломатлик ва уро-нефрологик тадқиқотлар журнали)
Nashr sanasi2022-10-27
Jild3
Son3
TilRus

Kalit so‘zlar

маточно–вагинальная аплазия, аплазия Майера-Рокитанского-Синдром-Кюстера-Хаузера, гипопластическим двусторонним придатком, первичная аменорея, uterovaginal aplasia, Mayer-Rokitansky-Kuester-Hauser syndrome, hypoplastic bilateral appendage, primary amenorrhea, utero-vaginal aplaziya, Mayer-Rokitanskiy aplaziyasi-sindromi, gipoplastik ikki tomonlama bachadon ortiqlari, birlamchi amenoreya

Ilmiy soha

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